Images in clinical medicine | Volume 40, Article 80, 06 Oct 2021 | 10.11604/pamj.2021.40.80.26009

Ectrodactyly-lobster claw deformity

Sarath Kumar Udaya Kumar, Krishna Prasanth Baalan

Corresponding author: Sarath Kumar Udaya Kumar, Department of Community Medicine, Sree Balaji Medical College and Hospital, Bharath University, India

Received: 10 Sep 2020 - Accepted: 16 Sep 2020 - Published: 06 Oct 2021

Domain: Pediatrics (general),Orthopedic surgery

Keywords: Deformity, children, congenital

©Sarath Kumar Udaya Kumar et al. Pan African Medical Journal (ISSN: 1937-8688). This is an Open Access article distributed under the terms of the Creative Commons Attribution International 4.0 License (https://creativecommons.org/licenses/by/4.0/), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.

Cite this article: Sarath Kumar Udaya Kumar et al. Ectrodactyly-lobster claw deformity. Pan African Medical Journal. 2021;40:80. [doi: 10.11604/pamj.2021.40.80.26009]

Available online at: https://www.panafrican-med-journal.com/content/article/40/80/full

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Images in clinical medicine

Ectrodactyly-lobster claw deformity

Ectrodactyly-lobster claw deformity

Sarath Kumar Udaya Kumar1,&, Krishna Prasanth Baalan1

 

1Department of Community Medicine, Sree Balaji Medical College and Hospital, Bharath University, Chennai, India

 

 

&Corresponding author
Sarath Kumar Udaya Kumar, Department of Community Medicine, Sree Balaji Medical College and Hospital, Bharath University, Chennai, India

 

 

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Lobster-claw deformity, also called as ectrodactyly is an uncommon congenital presentation occurring in the hand due to longitudinal failure of development of second, third or fourth ray. It occurs in 1 to 4 newborns in 100,000 live births. It occurs mostly due to consanguineous marriage but can also occur in the non - consanguineous marriage. This deformity is usually associated with ectodermal defects, mental retardation, deafness, orofacial clefting and tibial aplasia. A 6-year-old boy was brought to the Department of Orthopedics in a Private Medical Hospital, Chennai, with deformity of left hand since birth. The affected hand had a wide median cleft and, there was deformity of flexion of the ring and index finger with absence of middle finger. The other hand and both feet were normal. On radio-imaging, left hand showed transversely oriented bone between third and fourth metacarpal and phalanges of middle finger were absent except for rudimentary proximal phalanx. No other congenital defects were present other than this. The child was born to non-consanguineous parents with no significant family history. The treatment for this anomaly is complete surgical excision of transverse bone with partial excision of the third metacarpal and apposition of the second and fourth metacarpal by absorbable sutures which leads to a smaller cleft. If required, flexion contracture of ring and index finger will be corrected.

 

 

Figure 1: lobster claw deformity

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

Images in clinical medicine

Ectrodactyly-lobster claw deformity

Images in clinical medicine

Ectrodactyly-lobster claw deformity

Images in clinical medicine

Ectrodactyly-lobster claw deformity

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