A pulmonary aneurysm: donít forget Hughes-Stovin syndrome
Madiha Mahfoudhi, Sami Turki
The Pan African Medical Journal. 2015;20:445. doi:10.11604/pamj.2015.20.445.5938

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A pulmonary aneurysm: donít forget Hughes-Stovin syndrome

Cite this: The Pan African Medical Journal. 2015;20:445. doi:10.11604/pamj.2015.20.445.5938

Received: 13/12/2014 - Accepted: 22/12/2014 - Published: 30/04/2015

Key words: Pulmonary aneurysm, hemoptysis, Hughes-Stovin syndrome

© Madiha Mahfoudhi et al. The Pan African Medical Journal - ISSN 1937-8688. This is an Open Access article distributed under the terms of the Creative Commons Attribution License (http://creativecommons.org/licenses/by/2.0), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.

Available online at: http://www.panafrican-med-journal.com/content/article/20/445/full

Corresponding author: Madiha Mahfoudhi, Service de Mťdecine Interne A, HŰpital Charles Nicolle, Tunis, Tunisie (madiha_mahfoudhi@yahoo.fr)


A pulmonary aneurysm: donít forget Hughes-Stovin syndrome

 

Madiha Mahfoudhi1,&, Sami Turki1

 

1Service de Mťdecine Interne A, HŰpital Charles Nicolle, Tunis, Tunisie

 

 

&Corresponding author
Madiha Mahfoudhi, Service de Mťdecine Interne A, HŰpital Charles Nicolle, Tunis, Tunisie

 

 

Image in medicine

Hughes-Stovin syndrome is a scarce pathology associating pulmonary artery aneurysms and deep venous thrombosis and affecting commonly the young patient. A 27 year old man was hospitalised for recurrent hemoptysis and a left femoral vein thrombosis. Besides, he had oral ulcers. The ophthalmological examination was normal. Laboratory studies found a microcytic hypochromic anemia (hemoglobin: 11g/dl).The coagulation tests, the renal and the hepatic functions were normal. Besides, the bacteriological examination in search for mycobacterium tuberculosis and the immunological investigations were negative. The chest radiograph revealed a left surrounded para-hilar opacity. The CT of the chest confirmed the presence of a giant aneurysm in the left lower lobe pulmonary artery of 90 mm/72 mm, partially thrombosed, occupying the quasi-totality of the left pulmonary field. All abnormalities of hemostasis, a tumoral origin, a vasculitis like BehÁet's disease and an infectious etiology were eliminated in our patient. Therefore, Hughes-Stovin syndrome was our diagnosis. The patient was put on oral corticosteroid (1 mg/kg/day), and intravenous cyclophosphamide; the steroids were subsequently tapered and withdrawn after 6 months until reaching a minimal dose of 10 mg/day. There has been no recurrence of deep venous thrombosis or hemoptysis. There was no evidence of enlargement of the pulmonary artery aneurysms on chest CT scan control. He was programmed for an embolization because of the giant aspect of the aneurysm.

 

 

Figure 1: chestís CT: a giant aneurysm in the left lower lobe pulmonary artery, with mural thrombus

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 


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