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Cite this article:
Smael Labib, Mohamed Adnane Berdai, Sanae abourazzak, Mustapha Hida, Mustapha Harandou. Congenital insensitivity to pain with anhydrosis: report of a family case. The Pan African Medical Journal. 2011;9:33 Key words: Congenital insensitivity to pain, hereditary, neuropathy, sensory and autonomic neuropathy, family case, anesthesia Permanent link: http://www.panafrican-med-journal.com/content/article/9/33/full Received: 18/05/2011 - Accepted: 25/07/2011 - Published: 25/07/2011 © Smael Labib et al. The Pan African Medical Journal - ISSN 1937-8688. This is an Open Access article distributed under the terms of the Creative Commons Attribution License (http://creativecommons.org/licenses/by/2.0), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited. |
Congenital insensitivity to pain with anhydrosis: report of a family case
Smael Labib1,&, Mohamed Adnane Berdai1, Sanae abourazzak2, Mustapha Hida2, Mustapha Harandou1
1Department of anesthesia and intensive care, University Hospital Hassan II, Fez, Morocco, 2Department of Pediatrics, University Hospital Hassan II, Fez, Morocco
&Corresponding author
Smael Labib, Department of anesthesia and intensive care, University Hospital Hassan II, Fez, Morocco
Congenital Insensitivity to pain with anhydrosis (CIPA) is a rare inherited disease. It is classified as hereditary sensory and autonomic neuropathy type IV. Pain insensitivity and autonomic deficits are present, but touch and pressure sensitivity are unimpaired. Mental retardation is usually present. We report a family case of a 5 years old girl and 2 years old boy with congenital insensitivity to pain, while discussing the clinical features and the anesthetic strategy of such patients. Patients with Congenital Insensitivity to Pain with anhydrosis may undergo surgery because of susceptibility to trauma due to absence of pain. The clinical features may intrinsically possess anesthetic challenges.
