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Cite this article:
Faten Frikha, Makram Frigui, Hatem Masmoudi, Hamida Turki, Zouhir Bahloul. Systemic sclerosis in a patient with pityriasis rubra pilaris. The Pan African Medical Journal. 2010;6:6 Key words: Systemic sclerosis, pityriasis rubra pilaris, skin disease, autoimmune disease, acroosteolysis, rare diseases Permanent link: http://www.panafrican-med-journal.com/content/article/6/6/full Received: 22/06/2010 - Accepted: 05/08/2010 - Published: 09/08/2010 © Faten Frikha et al. The Pan African Medical Journal - ISSN 1937-8688. This is an Open Access article distributed under the terms of the Creative Commons Attribution License (http://creativecommons.org/licenses/by/2.0), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited. |
Systemic sclerosis in a patient with pityriasis rubra pilaris
Faten Frikha1,&, Makram Frigui1, Hatem Masmoudi2, Hamida Turki3, Zouhir Bahloul1
1Department of Internal Medicine, Hospital of Hedi Chaker, 3029 Sfax, Tunisia, 2Laboratory of Immunology, Hospital of Habib Bourguiba 3029 Sfax, Tunisia, 3Department Of Dermatology, Hospital of Hedi Chaker, 3029 Sfax, Tunisia
&Corresponding author
Faten Frikha, Service de Médecine interne CHU Hédi Chaker 3029 Sfax, Tel : +21698657098, Tunisia
Abstract
Pityriasis rubra pilaris (PRP) is a rare, chronic erythematous squamous disorder of unknown etiology. It has been found in association with several autoimmune diseases, including thyroiditis, myositis, myasthenia gravis and vitiligo. Herein we report a case of systemic sclerosis in a patient with classic adult pityriasis rubra pilaris. A 38 year old woman with classic adult type 1 pityriasis rubra pilaris (PRP) developed progressive skin thickening of the trunk, face, upper and lower extremities after 2 years of PRP treatment with topical emollients and steroids. Clinical examination and immunological findings were consistent with SSc. Co-existence of these two rare conditions is documented for the first time.
