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Cite this article:
Mahdi Kahrom, Hadi Kahrom. Scimitar syndrome and evolution of managements. The Pan African Medical Journal. 2009;3:20 Key words: Scimitar syndrome, anomalous pulmonary venous drainage, pulmonary venolobar syndrome, Dextrocardia Permanent link: http://www.panafrican-med-journal.com/content/article/3/20/full Received: 10/11/2009 - Accepted: 16/12/2009 - Published: 17/12/2009 © Mahdi Kahrom et al. The Pan African Medical Journal - ISSN 1937-8688. This is an Open Access article distributed under the terms of the Creative Commons Attribution License (http://creativecommons.org/licenses/by/2.0), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited. |
Scimitar syndrome and evolution of managements
Mahdi Kahrom 1,&, Hadi Kahrom1
1 Division of Cardiothoracic Surgery, Imam Reza Hospital, Mashhad University of Medical Sciences, Mashhad, Iran
&Corresponding author
Division of Cardiothoracic Surgery, Imam Reza Hospital, Mashhad University of Medical Sciences, Mashhad, Iran. Phone: +98-915-5017276. Fax: +98-511-8674939
Abstract
The Scimitar syndrome is a rare congenital anomaly that consists in part of total or partial anomalous venous drainage of the right lung to the inferior vena cava (IVC). This descending vein is visible on CXR as a curvilinear density along the right heart border and resembles the curved Turkish sword that gives the condition its name. Scimitar syndrome forms part of the large spectrum of associated conditions known as venolobar syndrome. These include right lung hypoplasia or sequestered segments of the right lung, congenital heart disease and various others. Surgical approaches to the Scimitar syndrome have varied according to the anatomic and pathologic features presented in each case. Here we review the clinical signs and symptoms, diagnostic dilemmas, current medical and surgical managements of Scimitar syndrome.
