Kartagener’s syndrome
Rodolfo Mendes Queiroz, Fred Bernardes Filho
The Pan African Medical Journal. 2018;29:160. doi:10.11604/pamj.2018.29.160.14927

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Kartagener’s syndrome

Cite this: The Pan African Medical Journal. 2018;29:160. doi:10.11604/pamj.2018.29.160.14927

Received: 21/01/2018 - Accepted: 26/02/2018 - Published: 19/03/2018

Key words: Kartagener´s syndrome, dextrocardia, sinusitis

© Rodolfo Mendes Queiroz et al. The Pan African Medical Journal - ISSN 1937-8688. This is an Open Access article distributed under the terms of the Creative Commons Attribution License (http://creativecommons.org/licenses/by/2.0), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.

Available online at: http://www.panafrican-med-journal.com/content/article/29/160/full

Corresponding author: Fred Bernardes Filho, Dermatology Division, Department of Medical Clinics, Ribeirão Preto Medical School, University of São Paulo, Ribeirão Preto, Brazil (f9filho@gmail.com)


Kartagener’s syndrome

Rodolfo Mendes Queiroz1,2, Fred Bernardes Filho3,&

 

1Department of Radiology and Imaging, Santa Casa da Misericórdia of Avaré, Avaré, São Paulo, Brazil, 2CENTROMED Diagnóstico por Imagem, Avaré, São Paulo, Brazil, 3Dermatology Division, Department of Medical Clinics, Ribeirão Preto Medical School, University of São Paulo, Ribeirão Preto, Brazil

 

 

&Corresponding author
Fred Bernardes Filho, Dermatology Division, Department of Medical Clinics, Ribeirão Preto Medical School, University of São Paulo, Ribeirão Preto, Brazil

 

 

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A 29-year-old non-smoker male with a history of chronic cough, and recurrent pneumonia, sinusitis and otomastoiditis was admitted to the emergency room with a 3-day history of headache, cough productive and dyspnea. Positive findings on physical examination included heart sounds in the right side of his chest and pain on palpation and percussion of the sinus areas. Laboratory testing was unremarkable. Chest radiography showed dextrocardia (A); computed tomography (CT) of the face showed mucosal thickening and material with soft tissue density in the paranasal sinuses, mastoid cells and in the middle and external ear cavities (B,C); chest CT showed bronchiectasis and centrilobular nodules (tree-in-bud pattern) (D,E); liver on the left and spleen on the right (F). The diagnosis of Kartagener's syndrome (KS) was made. KS is a subset of primary ciliary dyskinesia, an autosomal recessive condition characterised by bronchiectasis, paranasal sinusitis and situs inversus totalis (SIT). Patients with KS often have multiple episodes of respiratory tract infection and exacerbation of bronchiectasis due to poor mucociliary clearance and some male patients with KS also have sterility due to dyskinesia of the spermatozoa. Clinicians and mainly emergency physicians should be aware of this rare disorder once failure to recognize this syndrome can be potentially hazardous, especially in surgical conditions.

 

 

Figure 1: Kartagener’s syndrome: A) chest radiography with dextrocardia; B,C) face CT with mucosal thickening and material with soft tissue density in the paranasal sinuses, mastoid cells and in the middle and external ear cavities; D,E) axial chest CT showing bronchiectasis and centrilobular nodules (tree-in-bud sign); F) axial CT image showing liver (L) on the left and spleen (S) on the right

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 


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Keywords

Kartagener´s syndrome
Dextrocardia
Sinusitis

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